Malformasi Anorektal. Anorectal malformations comprise a wide spectrum of diseases, which can affect boys and girls, and involve the distal anus and rectum as well as the urinary. Anorectal malformations (ARMs) are among the more frequent congenital anomalies encountered in paediatric surgery, with an estimated incidence ranging.

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The enormously dilated rectosigmoid, with normal ganglion cells, behaves like a myopathic type of hypomotile colon. After colostomy closure, severe diaper rash is common because the perineal skin has never before been exposed to stool.

This is also true for female patients, not including the kalformasi group. The bladder neck in most patients is competent, and these patients that require catheterization remain dry in between. Colostomy type in anorectal malformations: Amussat, in was the first individual who sutured the rectal maoformasi to the skin edges, which could be considered the first anoplasty.

The anus must be dilated twice daily and every week the size of the dilator is increased. Important technical considerations and new applications. Ratto C, Doglietto GB, editor.

Continence after posterior sagittal anorectoplasty. Surgical procedure Understanding of anatomy and thus the principal of surgical repair of ARM has evolved continuously over the past century. In patients with imperforate anus without fistula, the same meticulous dissection is required to separate the distal rectum from the urinary tract as in patient with rectourinary fistulae because the rectum and urethra still share a common wall.


These features are externally visible and help diagnose a perineal fistula.

Bowel management is an artificial way to keep patients who have fecal incontinence clean. Treatment Surgery Anoreital discussed previously, the surgeon must decide in the newborn period whether the child requires fecal diversion with a colostomy, or can undergo a primary repair procedure.

This approach allowed surgeons to view the anatomy of these defects clearly, to repair them under direct vision, and to learn about the complex anatomic arrangement of the junction of the rectum and genitourinary tract. Urinary function The patients with ARM are frequently complicated with urinary tract anomalies or sacral anomalies.

Malformasi Anorektal | Lokananta | Jurnal Kedokteran Meditek

The surgeon may not be able to find the rectum and may find malforasi damage other, unexpected, structures, such as the posterior urethra, seminal vesicles, vas deferens, and ectopic ureter during the search for the rectum.

Decision-making for male newborns Male newborns with recto-perineal fistula do not need a colostomy. In particular, mutations in specific genes encoding transcription factors have been described in patients having Townes-Broks syndrome, Currarino’s syndrome, and Pallister-Hall syndrome, each of which have autosomal dominant modes of inheritance.

Normally, there are three visible openings — the most anterior being the urethra, followed by the vagina, both of these being within the vestibule.

Laparoscopy and its use in the repair of anorectal malformations.


Except for cloacas, in most cases of female malformations, distal colostography is not necessary because the fistula is malformwsi clinically. Ma,formasi radiographs of the spine can show spinal anomalies such as spina bifida and spinal hemivertebrae.

Advances in the imaging techniques with improvement in knowledge of the embryology, anatomy and physiology of ARM cases have refined diagnosis and initial management.

Received Jul 18; Accepted Jul Less frequently than constipation, some patients may experience soiling. Table 3b Krickenbeck classification of surgical procedures. Urologic evaluation prior to colostomy provides the surgeon the necessary information needed to address the urologic problem at the time of the colostomy.

Anorectal malformations

In cases with aborektal channels longer than 3 cm, it is difficult to mobilize the vagina through PSARP, and an abdominoperineal approach is required. Most of these patients have excellent sphincter mechanisms and a normal sacrum. Support Center Support Center. Very few long-term prospective studies have been performed to know the overall growth and development of ARM patients. Gross abdominal distension, sepsis, or single opening persistent cloaca warrants a diversion colostomy.

Anorectal Malformations in Children: It is performed with the patient positioned prone with the pelvis elevated; multiple fine silk sutures are places at the mucocutaneous junction of the bowel orifice for traction.