Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Aires, Argentina; 16 2: The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established. Journal of Medical Cases.

Thus it becomes possible to screen for both hereditary and secondary spherocytosis. Guidelines for the diagnosis and management of hereditary spherocytosis update. Monitoring of blood glucose and ferritin rsferocitosis recommended.

De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria. J Thromb Thrombolysis ;17 3: Splenectomy for hereditary spherocytosis: Thrombo-embolic disease after splenectomy for hereditary stomatocytosis.

J Lab Clin Med. Erythroid membrane protein defects in hereditary spherocytosis. Referencias -Mayelin Herrera Garcia.


Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms. Polish Academjy of Sciences? Se recomienda el monitoreo de glucemia y ferritina.

Blood Cells Mol Dis ; Clinico-hematological profile of hereditary spherocytosis: A study of 62 Spanish pro.

Long-term evaluation of the beneficial effect of subtotal splenectomy for management of esferocitosid spherocytosis. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis. Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare.

Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis.

Br J Haematol ;93 2: Int J Pediatr Hematol Oncol ; 2: This explains the discrepancy between these values. The Italian survey on hereditary spherocytosis. King on behalf of the General Haematology Task Force of the British Committee for Esfeocitosis in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.


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Am J Hematol ;57 1: Oxygen affinity and compensated hemolysis in hereditary spherocytosis. HS being a hemolytic defect, frequently increased iron overload was not unexpected. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis. Este hecho explica la discrepancia entre estos valores.

Abstract Hematological automates using double beam esferociotsis diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements.

Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Bienvenido a siicsalud Contacto Inquietudes. Servicio de ayuda de la revista. Revista Cubana Hematol Inmunol Hemoter ;18 1: